anti-CPS1 (human), Rabbit Monoclonal (RM395)

Product description: Carbamoyl phosphate synthetase I (CPS1 or CPSI) is a ligase enzyme located in the mitochondria involved in the production of urea. It transfers an ammonia molecule from glutamine or glutamate to a molecule of bicarbonate that has been phosphorylated by a molecule of ATP. The resulting carbamate is then phosphorylated with another molecule of ATP. The resulting molecule of carbamoyl phosphate leaves the enzyme. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. Mutations in this gene have been associated with carbamoyl phosphate synthetase 1 deficiency (CPS1D), susceptibility to persistent pulmonary hypertension and susceptibility to venoocclusive disease after bone marrow transplantation.

Alternate Names/Synonyms: Carbamoyl-phosphate Synthase 1; CPSase1

Product Type: Recombinant Antibody

Clone: RM395

Isotype: Rabbit IgG

Immunogen: A peptide corresponding to Human CPS1.

Applications: IHC, WB

Species Crossreactivity: Human

Specificity: This antibody reacts to human CPS1.

Concentration: N/A

Long Term Storage: -20°C

Shipping: BLUE ICE

Use & Stability: Stable for at least 1 year after receipt when stored at -20°C.

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